As comunicações interventriculares (CIV), na forma isolada, são, de longe, a comunicação interventricular com atresia pulmonar (CIV/AP), a transposição das . La atresia pulmonar es una enfermedad del corazón presente ya en el momento del nacimiento, por lo que se incluye dentro del grupo de enfermedades. Atresia Pulmonar con Septo Interventricular cerrado. Doble Emergencia del pulmonar a la prueba de oxígeno: Cierre de CIV o Si RPT > 7 uds y posible.

Author: Nazshura Akilkis
Country: Brunei Darussalam
Language: English (Spanish)
Genre: Finance
Published (Last): 4 May 2011
Pages: 254
PDF File Size: 2.44 Mb
ePub File Size: 1.11 Mb
ISBN: 499-3-24448-500-9
Downloads: 7249
Price: Free* [*Free Regsitration Required]
Uploader: Sharg

Clinical relevance afresia monosomy 22q The mortality presented a greater correlation with the morphologic characteristics than with the morphometric characteristics. Incidence and significance of 22q Recognizing a common genetic syndrome: J Am Coll Cardiol ; Staged repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries: The indices of the patients who died were lower that those who survived, however, the differences were not statistically significant.

Br Heart J ; Genetic analyses in two extended families with deletion div syndrome: Correlation between the A, B and C groups, their indices and treatment stages.

Philadelphia, WB Saunders, ; Of these, four also presented with stenosis of the right pulmonary artery and only one achieved DT, showing that the presence of stenosis in both the CPA is an important factor in pulmoonar to surgical correction [12]. Thus, with basis in the analysis of cine angiocardiograms of patients suffering from PA with VSD, the present study aims at identifying within the groups proposed by the Barbero-Marcial classification, subgroups with pulmonary vascular blood supplies that present similar morphological characteristics, to assess their CPA and MAPCA, to attempt to establish implications involved in surgical treatment.


Introduction Pulmonad atresia PA with ventricular septal defect VSD is defined as a group of cardiopulmonary malformations of coni-truncal origin, in which there is an interruption in the continuity of the lumen and absence of blood flow ci the ventricles and the central pulmonary arteries CPA. Am J Med Genet ; In a biventricular heart pulmohar presents with an orifice in the interventricular septum [1].

Chromosome 22q11 microdeletions in tetralogy of Fallot. The incidence of a deletion in chromosome 22Q11 in sporadic and familial conotruncal heart disease. The morphological characteristics were more important and significant for the choice of treatment.

Analysis of group B The cardiac cineangiographic studies of all the patients of this group were submitted to morphometric analysis as can be seen in Table 2. Results Of the total of 63 patients, 15 Pulmohar, there was no statistical difference between group C1 and C2 in relation to the procedures performed.

Atresia pulmonar

Information was obtained from medical records and referring physicians. Rev Assoc Med Bras ; There was no association among the numbers of MAPCA, the presence of stenosis and the treatment stages.

The same can be said in respect to the B2 and B4 subgroups.

Chromosome 10p and 22q11 deletion screening in patients with isolated and syndromic conotruncal heart defects. The median age at the first cardiac cineangiographic study was 1. In the patients with complete repair, the median right-to-left ventricle pressure ratio cig 0. Commonly this is seen with a microdeletion of atrssia long arm of chromosome 22 q The morphological and morphometric characteristics allow suggestions for the surgical therapy, as the patients from group A have a greater chance of definitive treatment, those of group B of palliative treatment and those of group C of definitive palliative treatment.


Similarly, Reddy et al. Clinical features of chromosome 22q Influence of chromosome 22q A search for chromosome 22q Defeitos do septo interventricular, cirurgia. Knowing the weight and height of the patients at the moment of the examination, the body surface was calculated utilizing Mosteller’s formula [11]. Eur J Cardiothorac Surg ; Schematic representation of the B1 subgroup with central pulmonary arteries supplying the left superior and right inferior lobes.

The profile and outcome of patients admitted to a pediatric intensive care unit. J Paediatr Child Health ; Chromosome abnormalities in congenital heart disease.

Atresia pulmonar – Wikipedia, la enciclopedia libre

Clin Chim Acta ; The mortality of disease in this subgroup of patients was Typical phenotypic spectrum of velocardiofacial syndrome occurs independently of deletion size in chromosome 22q J Thorac Cardiovasc Surg ; Medline, Lilacs and SciELO databases were searched from to using specific descrip-tors as “22q11”, “DiGeorge syndrome”, “velocardiofacial syndrome”, “congenital heart defects” and “cardiovascular malformations”. New York, Churchill- Livingstone, ; The fate of children with microdeletion 22q Rosa I ; Paulo Ricardo G.

In subgroup A2 there was a greater number of patients who required two procedures than in subgroup A1.